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Issue Date
2003-12-01
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Pulmonary sequestration - a case report and review of the litteratureCitation
Læknablaðið 2003, 89(12):949-52Abstract
Pulmonary sequestration is an uncommon congenital malformation where non-functioning lung tissue is separated from the normal bronchopulmonary tree and vascularized by an aberrant systemic artery. We describe a previously healthy 17 year old girl who was diagnosed with intralobar sequestration following a pneumonia and pulmonary abscess. The diagnosis was made with on CT-scan and confirmed by MRI angiography. A right lower lobectomy was performed and six months later the patient was without symptoms. The case is discussed and the literature reviewed.Aðskilinn lungnahluti er sjaldgæfur meðfæddur galli þar sem hluti lungna er án tengsla við lungnaberkjur og lungnablóðrás. Lungnahlutinn tekur því ekki þátt í loftskiptum. Oftar en ekki veldur aðskilinn lungnahluti einkennum, oftast lungnasýkingum. Sjúklingarnir geta einnig verið án einkenna og greinast stundum fyrir tilviljun. Hér er lýst áður hraustri 17 ára gamalli stúlku sem greindist með aðskilinn lungnahluta í kjölfar lungnabólgu og ígerðar í hægra lunga. Greining fékkst með tölvusneiðmyndatöku og segulómun. Lungnahlutinn var fjarlægður með opinni skurðaðgerð og var staðsettur í neðra blaði lungans. Tæpu ári eftir aðgerðina er sjúklingurinn einkennalaus og við góða heilsu.
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